Intrarenal arterial aneurysms with haematuria in a patient with tuberous sclerosis complex.

Tuberous sclerosis complex (TSC) is an autosomal dominant disease with a wide spectrum of pathological lesions [1,2]. Almost half of the patients with TSC have an underlying renal pathology, mainly angiomyolipomas, cysts and/or renal cell carcinoma [3,4]. TSC rarely involves medium size and large vessels, including the renal arteries. Arterial aneurysms have been reported for intracranial arteries, for the aorta and for the kidneys in patients with TSC [5]. The clinical management of the two main complications, fever and haematuria, in these patients is uncertain. Here we report on a patient with two large intrarenal arterial aneurysms who presented with macroscopic haematuria and fever successfully treated by intraarterial embolization.